INTERNATIONAL CLASSIFICATION OF DISEASES

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272 Disorders of lipoid metabolism

          Excludes: localized cerebral lipidoses (330.1)

272.0 Pure hypercholesterolemia

          Familial hypercholesterolemia
          Fredrickson's Type IIa hyperlipoproteinemia
          Hyper-beta-lipoproteinemia
          Hyperlipidemia, Group A
          Low-density-lipoid-type [LDL] hyperlipoproteinemia

272.1 Pure hyperglyceridemia

          Endogenous hyperglyceridemia
          Fredrickson's Type IV hyperlipoproteinemia
          Hyperlipidemia, Group B
          Hyper-pre-beta-lipoproteinemia
          Hypertriglyceridemia, essential
          Very-low-density-lipoid-type [VLDL] hyperlipoproteinemia

272.2 Mixed hyperlipidemia

          Broad- or floating-beta-lipoproteinemia
          Fredrickson's Type IIb or III hyperlipoproteinemia
          Hypercholesterolemia with endogenous hyperglyceridemia
          Hyper-beta-lipoproteinemia with pre-beta-lipoproteinemia
          Hyperlipidaemia, Group C
          Tubo-eruptive xanthoma
          Xanthoma tuberosum

272.3 Hyperchylomicronemia

          Fredrickson's type I or V Hyperlipidemia, Group D
           hyperlipoproteinemia Mixed hyperglyceridemia

272.4 Other and unspecified hyperlipidemia

          Alpha-lipoproteinemia Hyperlipidemia NOS
          Combined hyperlipidemia

272.5 Lipoprotein deficiencies

          A-beta-lipoproteinemia Hypo-beta-lipoproteinemia (familial
          High-density lipoid deficiency Lecithin cholesterol acyltransferase
          Hypo-alpha-lipoproteinemia deficiency
           Tangier disease

272.6 Lipodystrophy

          Barraquer-Simons disease Progressive lipodystrophy
          Use additional E code, if desired, to identify cause, if iatrogenic
          Excludes: intestinal lipodystrophy (040.2)

272.7 Lipidoses

          Chemically induced lipidosis Disease:
          Disease: pseudo-Hurler's or mucolipidosis III
           Anderson's Sandhoff's
           Fabry's triglyceride-storage, Type I or II
           Gaucher's Wolman's or triglyceride-storage,
           I-cell or mucolipidosis I Type III
           lipoid-storage NOS Mucolipidosis II
           Niemann-Pick Primary familial xanthomatosis

272.8 Other disorders of lipoid metabolism

          Hoffa's disease or liposynovitis prepatellaris
          Launois-Bensaude's lipomatosis

272.9 Unspecified disorders of lipoid metabolism

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INTERNACIONAL CLASSIFICATION OF DISEASES