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272 Disorders of lipoid metabolism
Excludes: localized cerebral lipidoses (330.1)
272.0 Pure hypercholesterolemia
Familial hypercholesterolemia
Fredrickson's Type IIa hyperlipoproteinemia
Hyper-beta-lipoproteinemia
Hyperlipidemia, Group A
Low-density-lipoid-type [LDL] hyperlipoproteinemia
272.1 Pure hyperglyceridemia
Endogenous hyperglyceridemia
Fredrickson's Type IV hyperlipoproteinemia
Hyperlipidemia, Group B
Hyper-pre-beta-lipoproteinemia
Hypertriglyceridemia, essential
Very-low-density-lipoid-type [VLDL] hyperlipoproteinemia
272.2 Mixed hyperlipidemia
Broad- or floating-beta-lipoproteinemia
Fredrickson's Type IIb or III hyperlipoproteinemia
Hypercholesterolemia with endogenous hyperglyceridemia
Hyper-beta-lipoproteinemia with pre-beta-lipoproteinemia
Hyperlipidaemia, Group C
Tubo-eruptive xanthoma
Xanthoma tuberosum
272.3 Hyperchylomicronemia
Fredrickson's type I or V Hyperlipidemia, Group D
hyperlipoproteinemia Mixed hyperglyceridemia
272.4 Other and unspecified hyperlipidemia
Alpha-lipoproteinemia Hyperlipidemia NOS
Combined hyperlipidemia
272.5 Lipoprotein deficiencies
A-beta-lipoproteinemia Hypo-beta-lipoproteinemia (familial
High-density lipoid deficiency Lecithin cholesterol acyltransferase
Hypo-alpha-lipoproteinemia deficiency
Tangier disease
272.6 Lipodystrophy
Barraquer-Simons disease Progressive lipodystrophy
Use additional E code, if desired, to identify cause, if iatrogenic
Excludes: intestinal lipodystrophy (040.2)
272.7 Lipidoses
Chemically induced lipidosis Disease:
Disease: pseudo-Hurler's or mucolipidosis III
Anderson's Sandhoff's
Fabry's triglyceride-storage, Type I or II
Gaucher's Wolman's or triglyceride-storage,
I-cell or mucolipidosis I Type III
lipoid-storage NOS Mucolipidosis II
Niemann-Pick Primary familial xanthomatosis
272.8 Other disorders of lipoid metabolism
Hoffa's disease or liposynovitis prepatellaris
Launois-Bensaude's lipomatosis
272.9 Unspecified disorders of lipoid metabolism
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