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286 Coagulation defects
286.0 Congenital factor VIII disorder
Factor VIII (functional) Hemophilia:
deficiency NOS
A
Excludes: factor VIII deficiency with vascular defect (286.4)
286.1 Congenital factor IX disorder
Christmas disease Hemophilia B
Deficiency:
factor IX (functional)
plasma thromboplastin component [PTC]
286.2 Congenital factor XI deficiency
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
286.3 Congenital deficiency of other clotting factors
Congenital afibrinogenemia Deficiency:
Deficiency of factor: AC globulin
I or fibrinogen proaccelerin
II or prothrombin Disease:
V or labile Owren's
VII or stable Stuart-Prower
X or Stuart-Prower Dysfibrinogenemia (congenital)
XII or Hageman Hypoproconvertinemia
XIII or fibrin stabilizing
286.4 von Willebrand's disease
Angiohemophilia
Factor VIII deficiency with vascular defect
Vascular hemophilia
Excludes: factor VIII deficiency:
NOS (286.0)
with functional defect (286.0)
hereditary capillary fragility (287.8)
286.5 Hemorrhagic disorder due to circulating anticoagulants
Hyperheparinemia
Increase in:
anti-VIIIa
anti-IXa
anti-Xa
anti-XIa
antithrombin
Systemic lupus erythematosus inhibitor
Use additional E code, if desired, to identify any administered anticoagulant
286.6 Defibrination syndrome
Afibrinogenemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation
Fibrinolytic hemorrhage, acquired
Purpura:
fibrinolytic
fulminans
Excludes: complicating abortion, pregnancy or the puerperium
(634-638 with fourth digit .1, 639.1, 641.3, 666.3)
disseminated intravascular coagulation in newborn (776.2)
286.7 Acquired coagulation factor deficiency
Deficiency of coagulation factor due to:
liver disease
vitamin K deficiency
Excludes: vitamin K deficiency of newborn (776.0)
286.9 Other and unspecified coagulation defects
Defective coagulation NOS
Deficiency, coagulation factor NOS
Delay, coagulation
Disorder:
coagulation
hemostasis
Prolongation of time of:
bleeding
coagulation
Excludes: complicating abortion, pregnancy or the puerperium
(634-638 with fourth digit .1, 639.1, 641.3, 666.3)
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