INTERNATIONAL CLASSIFICATION OF DISEASES

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286 Coagulation defects

286.0 Congenital factor VIII disorder

          Factor VIII (functional) Hemophilia:
           deficiency NOS
           A
          Excludes: factor VIII deficiency with vascular defect (286.4)

286.1 Congenital factor IX disorder

          Christmas disease Hemophilia B
          Deficiency:
           factor IX (functional)
           plasma thromboplastin component [PTC]

286.2 Congenital factor XI deficiency

          Hemophilia C
          Plasma thromboplastin antecedent [PTA] deficiency

286.3 Congenital deficiency of other clotting factors

          Congenital afibrinogenemia Deficiency:
          Deficiency of factor: AC globulin
           I or fibrinogen proaccelerin
           II or prothrombin Disease:
           V or labile Owren's
           VII or stable Stuart-Prower
           X or Stuart-Prower Dysfibrinogenemia (congenital)
           XII or Hageman Hypoproconvertinemia
           XIII or fibrin stabilizing

286.4 von Willebrand's disease

          Angiohemophilia
          Factor VIII deficiency with vascular defect
          Vascular hemophilia
          Excludes: factor VIII deficiency:
           NOS (286.0)
           with functional defect (286.0)
           hereditary capillary fragility (287.8)

286.5 Hemorrhagic disorder due to circulating anticoagulants

          Hyperheparinemia
          Increase in:
           anti-VIIIa
           anti-IXa
           anti-Xa
           anti-XIa
           antithrombin
          Systemic lupus erythematosus inhibitor
          Use additional E code, if desired, to identify any administered anticoagulant

286.6 Defibrination syndrome

          Afibrinogenemia, acquired
          Consumption coagulopathy
          Diffuse or disseminated intravascular coagulation
          Fibrinolytic hemorrhage, acquired
          Purpura:
           fibrinolytic
           fulminans
          Excludes: complicating abortion, pregnancy or the puerperium
           (634-638 with fourth digit .1, 639.1, 641.3, 666.3)
           disseminated intravascular coagulation in newborn (776.2)

286.7 Acquired coagulation factor deficiency

          Deficiency of coagulation factor due to:
           liver disease
           vitamin K deficiency
          Excludes: vitamin K deficiency of newborn (776.0)

286.9 Other and unspecified coagulation defects

          Defective coagulation NOS
          Deficiency, coagulation factor NOS
          Delay, coagulation
          Disorder:
           coagulation
           hemostasis
          Prolongation of time of:
           bleeding
           coagulation
          Excludes: complicating abortion, pregnancy or the puerperium
           (634-638 with fourth digit .1, 639.1, 641.3, 666.3)
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INTERNACIONAL CLASSIFICATION OF DISEASES